Chyluria results from the passage of lymph into the urine via abnormal
lymphaticourinary communications at the level of kidney, ureter or bl
adder. While filariasis is the most common cause of chyluria in tropic
al endemic areas congenital anomalies or obstructions of the lymphatic
duct predominate in Europe. This report describes symptoms as well as
diagnostic and therapeutic procedures in a 12-year-old boy with chylu
ria caused by a congenital fistula between lymphatic system and the bl
adder. Conclusions: In case of ''milky'' urine chyluria should be cons
idered as differential diagnosis. Lymphangiography is the most importa
nt diagnostic procedure to demonstrate the site of leakage. Obstructio
ns of the lymphatic system caused by filiasis, tuberculosis and tumors
have to be excluded. Chyluria without concurrent weightless, hypoalbu
minemia, anemia and colics should be treated conservatively.