TOTAL ANOMALOUS PULMONARY VENOUS CONNECTION TO THE PORTAL-VEIN

Anomalous pulmonary venous return represents a rare congenital anomaly with wide anatomic and physiologic variability. We report a case of a newborn with a rare form of total infracardiac anomalous pulmonary ve nous connection (TAPVC). The pulmonary veins draining both lungs forme d two vertical veins, which joined to a common pulmonary trunk below t he diaphragm. This venous channel connected to the portal vein through the esophageal hiatus. The diagnosis was suggested by color Doppler s onography and confirmed by intravenous digital subtraction angiography , which allowed definition of the anatomy.