HEPATIC-FIBROSIS WITH ADULT POLYCYSTIC KI DNEY AND LIVER-DISEASE

Objective: A case of hepatic fibrosis in adult polycystic liver diseas e is reported. This association, commonly present in infancy, is excep tional in the adult polycystic liver disease. Patient: We report a 69- years-old female with adult polycystic kidney and liver disease with f atal hepatic failure, portal hypertension and renal failure. An autops y was performed showing hepatic and renal polycystic disease with hepa tic fibrosis. Conclusion: Hepatic fibrosis is a rarely associated phen omenon with adult polycystic liver disease. This data may suggest a re lation of this entity with infancy fibropolycystic liver disease.