Extra-adrenal pheochromocytoma are extremely uncommon tumors. They dem
onstrate abdominal (97 % of the cases), thoracic, vesical or cervical
localizations. We report the case of a hepatic pheochromocytoma in a y
oung patient with a post history of labile arterial hypertension. Ultr
asonography, computed tomography and magnetic resonance imaging featur
es were similar to those of adrenal pheochromocytoma. The presence of
neuroendocrine cells was supported by immunohistochemical criteria. Hi
stological observation showed a lack of local extension. In addition,
four years after surgery, there was no apparent clinical syndrome sugg
esting tumor recurrence or metastasis occurrence. These observations s
upports the diagnosis of non malignant, primary hepatic pheochromocyto
ma. To our knowledge, this is the first radiologic description of this
kind of tumor.