SYSTEMIC VASCULITIS COMPLICATING INFANTILE AUTOIMMUNE ENTEROPATHY

Citation
Hr. Jenkins et al., SYSTEMIC VASCULITIS COMPLICATING INFANTILE AUTOIMMUNE ENTEROPATHY, Archives of Disease in Childhood, 71(6), 1994, pp. 534-535
Citations number
3
Categorie Soggetti
Pediatrics
ISSN journal
00039888
Volume
71
Issue
6
Year of publication
1994
Pages
534 - 535
Database
ISI
SICI code
0003-9888(1994)71:6<534:SVCIAE>2.0.ZU;2-P
Abstract
An infant with unexplained sideroblastic anaemia and severe protracted diarrhoea due to autoimmune gut disease is reported. Despite treatmen t with an exclusion diet and immunosuppressive agents she developed a severe systemic vasculitic illness. Intensive treatment with plasmapho resis resulted in resolution of the vasculitic process but the child s ubsequently died after overwhelming septicaemia.