PURPOSE/METHODS: The case of a 7-month-old infant illustrates the diag
nostic findings, including magnetic resonance imaging, and the difficu
lties of treating congenital corneal anesthesia. RESULTS/CONCLUSIONS:
The diagnosis of sporadic idiopathic congenital corneal anesthesia was
one of exclusion. Normal gasserian ganglia were demonstrated on magne
tic resonance imaging. Visual rehabilitation was successful with conti
nuous lubrication, arm splinting at bedtime, and treatment of amblyopi
a. It continues to be essential for the parents to monitor the corneal
status.