RETROPERITONEAL CASTLEMANS DISEASE - A NE W CASE-REPORT

A retroperitoneal localization of Castleman's disease was characterize d by angiolymphoid hyperplasia. This rare disease (58 cases of abdomin al localization reported to date) raises a question of nosology. The c linical features are not specific. Localized forms in young patients i nvolve deep lymph nodes and have a good prognosis after complete surgi cal exeresis. Inversely, the clinical picture is much more aggressive in multiple localizations involving preferentially superficial nodes w ith associated plasmocyte proliferation. The prognosis is mediocre in these forms. Although transition stages have been described due to the lack of any known aetiology, the question of nosology remains open: s hould the different forms be separated or identified simply as two pat hological forms?