UNRESECABLE HEPATIC HEMANGIOMA AND KASABA CH-MERRITT SYNDROME

The Kasabach-Merritt syndrome was first described in children with cut aneous hemangiomas, but it can exceptionally be associated with viscer al hemangiomas, especially in adults. Clotting and fibrinolysis within the hemangioma are thought to cause the coagulopathy observed in the so-called Kasabach-Merrit syndrome. This localised from of intra-vascu lar coagulation can progress to a secondary increased systemic fibrino lysis with fatal outcome for 20 to 30% of the patients. A transient co ntrol of hematologic abnormalities can frequently be obtained with blo od product support (platelets, fibrinogen, fresh plasma, cryoprecipita tes) and heparinotherapy. But in the adult, the only radical alternati ve is surgical excision if technically feasible. We reported here the case of a 43 year-old woman with a giant unresecable hepatic hemangiom a complicated with a Kasabach-Merrit syndrome.