SOLOMON SYNDROME WITH CORPUS-CALLOSUM AGENESIS AND MYOCARDIOPATHY

Solomon syndrome is peculiar in that it consists of the association of epidermal nevi with visceral abnormalities. It is always sporadic and must be distinguished from syndromes with epidermolytic epidermal nev i, which require a distinct approach as far as genetic counselling in concerned. We report a case associating sebaceous nevus, myocardiopath y and corpus callosa agenesia. Myocardiopathy has never been reported as being associated and there is only one case of corpus callosa agene sia in association with epidermal nevus in the literature.