The scimitar syndrome is a congenital anomaly that consists mainly of
total or partial anomalous venous drainage of the right lung to the in
ferior vena cava. We report the case of an 8-year-old girl diagnosed a
t birth as having a scimitar syndrome and who presented with recurrent
right lower lung infections. She underwent resection of the lower hal
f of her right lung without diversion of the anomalous venous drainage
of the upper portion of the lung. She improved rapidly postoperativel
y and the shunt fraction diminished.