MYOSITIS-OSSIFICANS PROGRESSIVA

Background. - Myositis ossificans progressiva is a rare progressive di sease of connective tissue with a poor prognosis. Case report. - A 16 year-old girl suffered from lameness of her right leg associated with inguinal swelling. Progressive aggravation of pain with extension of s welling to the posterior part of her high required an X ray examinatio n which showed hip dysplasia and calcifications around the hip. Angiog raphy was normal; a diagnosis of hematoma was suggested by scannograph y and bone scintigraphy, but biopsy showed features of nodular fasciit is. The association of progressive ectopic ossification to malformatio n of the big toe led to diagnosis of myositis ossificans progressiva. Conclusions. - Congenital malformations, most commonly of big toes and thumbs, are important for distinguishing myositis ossificans progress iva from other diseases of muscle.