HEMIMEGALENCEPHALY, HEMIHYPERTROPHY AND VASCULAR-LESIONS

We report on two children with hemihypertrophy and ipsilateral hemimeg alencephaly. Vascular lesions in one were consistent with a diagnosis of the Klippel-Trenaunay-Weber Syndrome. MRI performed in the first da ys of life and at 1 month of age revealed the presence of the neuronal anomaly. Conclusion The occurrence of hemimegalencephaly in our patie nts indicates that hemihypertrophy and vascular dysplasia are pathogen etically related phenomena of a continuous spectrum in which this brai n disorder may appear.