HEARING LEVELS IN PIERRE ROBIN-SYNDROME

Hearing was tested in 18 patients with Pierre Robin syndrome (PRS), Th ese results were compared with those obtained for 243 patients with ei ther cleft lip or cleft palate, or both. None of the PRS group patient s had middle ear or inner ear malformations, or sensorineural hearing loss in speech frequencies. Hearing loss in PRS is usually conductive, bilateral, and more frequent in PRS patients (30 ears or 83.33%) than in patients who do not have PRS (290 ears or 59.67%). A significantly higher (p < .01) mean of hearing loss for air conduction in speech fr equencies (MHLSF = 24.5 dB) was found in PRS patients than in patients without PRS (MHLSF = 17.8 dB), The ears of the PRS patients with hear ing loss were examined, revealing middle ear effusion, In all cases, h earing was restored to a normal level through suction and the use of v entilation tubes.