MALIGNANCY IN MAFFUCCI-SYNDROME

Authors
ALBREGTS AE RAPINI RP
Citation
Ae. Albregts et Rp. Rapini, MALIGNANCY IN MAFFUCCI-SYNDROME, Dermatologic clinics, 13(1), 1995, pp. 73-78
Citations number
NO
Categorie Soggetti
Dermatology & Venereal Diseases
Journal title
Dermatologic clinics → ACNP
ISSN journal
07338635
Volume
13
Issue
1
Year of publication
1995
Pages
73 - 78
Database
ISI
SICI code
0733-8635(1995)13:1<73:MIM>2.0.ZU;2-K
Abstract
Maffuci's syndrome is characterized by multiple enchondromas and subcu taneous hemangiomas. These tumors typically present in early childhood and may lead to significant skeletal deformities. Malignant transform ations are a common feature of this syndrome and have been reported in approximately 30% of reported cases, with chondrosarcomas being the m ost common.