A 37-year-old woman presented with acute left-sided proptosis. Magneti
c resonance imaging demonstrated a solid intraconal mass lesion with a
n associated 'capping' cyst. This lesion was resected and found on his
tological examination to be an optic nerve sheath meningioma. Small pe
rineural cysts have been reported with optic nerve sheath meningioma b
ut we believe this to be the ;first reported case of a large peritumor
al cyst associated ,vith this type of mass lesion. We speculate on the
aetiology of the cyst and the associated acute proptosis.