P. Ravasse et al., CYSTIC RETROPERITONEAL LYMPHANGIOMA - VAR IED CLINICAL PRESENTATION -REPORT OF 3 CASES, Archives de pediatrie, 2(3), 1995, pp. 232-236
Background. - Cystic retroperitoneal lymphangioma is a rare benign tum
or with varied clinical presentation. Case reports. - Case 1. A girl w
as born at term after ultrasonography had shown a cystic abdominal mas
s by 31 weeks of GA. This mass, clinically palpable at birth, was foun
d again by ultrasonography. Surgical excision on day 3 was incomplete,
requiring a second excision at the age of 2 months, followed by persi
stence of the cyst near the bladder; the patient was asymptomatic at t
he age of 2 years. Case 2. This full-term female newborn was admitted
because of jaundice and pallor. Examination showed a firm mass of the
left flank that was confirmed by X-rays and ultrasonography. Despite b
lood transfusion, anemia persisted, requiring surgery that showed a cy
stic hemorrhagic mass that was voided. A second partial excision was p
erformed a few weeks later and, at the age of 7 months, ultrasonograph
y showed a few small cystic masses behind the left kidney. Case 3. A 1
6-month-old boy was operated on for right inguinal hernia. The hernial
sac contained fluid and its wall was thick. Ultrasonography and CT sc
an performed 3 days later were normal. The child was examined again 28
months later because he suffered from abdominal pain; a large mass wa
s palpable in the right flank that appeared cystic at ultrasonography
and CT scan. A retroperitoneal lymphangioma was completely excised. Co
nclusion. - Because the risk of complications is apparently high, surg
ical treatment is always necessary. In the newborn period, complete ex
cision is difficult, requiring delayed surgery.