CYSTIC RETROPERITONEAL LYMPHANGIOMA - VAR IED CLINICAL PRESENTATION -REPORT OF 3 CASES

Citation
P. Ravasse et al., CYSTIC RETROPERITONEAL LYMPHANGIOMA - VAR IED CLINICAL PRESENTATION -REPORT OF 3 CASES, Archives de pediatrie, 2(3), 1995, pp. 232-236
Citations number
15
Categorie Soggetti
Pediatrics
Journal title
ISSN journal
0929693X
Volume
2
Issue
3
Year of publication
1995
Pages
232 - 236
Database
ISI
SICI code
0929-693X(1995)2:3<232:CRL-VI>2.0.ZU;2-K
Abstract
Background. - Cystic retroperitoneal lymphangioma is a rare benign tum or with varied clinical presentation. Case reports. - Case 1. A girl w as born at term after ultrasonography had shown a cystic abdominal mas s by 31 weeks of GA. This mass, clinically palpable at birth, was foun d again by ultrasonography. Surgical excision on day 3 was incomplete, requiring a second excision at the age of 2 months, followed by persi stence of the cyst near the bladder; the patient was asymptomatic at t he age of 2 years. Case 2. This full-term female newborn was admitted because of jaundice and pallor. Examination showed a firm mass of the left flank that was confirmed by X-rays and ultrasonography. Despite b lood transfusion, anemia persisted, requiring surgery that showed a cy stic hemorrhagic mass that was voided. A second partial excision was p erformed a few weeks later and, at the age of 7 months, ultrasonograph y showed a few small cystic masses behind the left kidney. Case 3. A 1 6-month-old boy was operated on for right inguinal hernia. The hernial sac contained fluid and its wall was thick. Ultrasonography and CT sc an performed 3 days later were normal. The child was examined again 28 months later because he suffered from abdominal pain; a large mass wa s palpable in the right flank that appeared cystic at ultrasonography and CT scan. A retroperitoneal lymphangioma was completely excised. Co nclusion. - Because the risk of complications is apparently high, surg ical treatment is always necessary. In the newborn period, complete ex cision is difficult, requiring delayed surgery.