INTESTINAL LYMPHANGIECTASIA IN A PATIENT WITH AUTOIMMUNE POLYGLANDULAR DISEASE TYPE-I AND STEATORRHEA

Authors
BEREKET A LOWENHEIM M BLETHEN SL KANE P WILSON TA
Citation
A. Bereket et al., INTESTINAL LYMPHANGIECTASIA IN A PATIENT WITH AUTOIMMUNE POLYGLANDULAR DISEASE TYPE-I AND STEATORRHEA, The Journal of clinical endocrinology and metabolism, 80(3), 1995, pp. 933-935
Citations number
22
Categorie Soggetti
Endocrynology & Metabolism
Journal title
The Journal of clinical endocrinology and metabolism → ACNP
ISSN journal
0021972X
Volume
80
Issue
3
Year of publication
1995
Pages
933 - 935
Database
ISI
SICI code
0021-972X(1995)80:3<933:ILIAPW>2.0.ZU;2-7
Abstract
Steatorrhea is seen in 18-24% of patients with autoimmune polyglandula r disease (APD) type 1. The etiology and pathophysiology of the steato rrhea in this disease are unknown. We present a patient with APD type 1 and steatorrhea in whom biopsies revealed intestinal lymphangiectasi a. This association has not been previously described. Intestinal lymp hangiectasia may explain the steatorrhea in some patients with APD typ e 1. As blind intestinal biopsies may miss areas of intestinal lymphan giectasia, endoscopically directed intestinal biopsies should be inclu ded in the evaluation of steatorrhea in APD type 1.