Proptosis, decreased vision and oculo-motor palsies developed in the l
eft eye of a 14-year-old girl, without neurofibromatosis signs. Comput
ed tomographic (CT) Scans of the head and orbit showed a large fusifor
m expansion of the left optic nerve without intracranial involvement.
Magnetic resonance imaging improved contrast resolution over CT Scanni
ng. A neurosurgical approach was performed and the optic nerve was res
ected from the back of the globe to the intracranial portion. Microsco
pic sections demonstrated oligodendroglioma, an unusual form of optic
nerve glioma.