We present a case of Netherton disease, where the hairs lacked the cha
racteristic microscopic feature of trichorrhexis invaginata. In its pl
ace were certain hairs with a golf tee morphology. These represent the
proximal half of the invaginate node seen in typical Netherton diseas
e. Scanning electron microscopy demonstrated the three-dimensional qua
lity of this abnormality, which is subtle when assessed by light micro
scopy alone. We describe this sign so that it might be recognized when
seen in isolation, as here, and allow the diagnosis of Netherton dise
ase to be confirmed.