ADULT RHABDOMYOMA - PRESENTATION AS A CERVICOMEDIASTINAL MASS (CASE-REPORT AND REVIEW OF THE LITERATURE)

The adult rhabdomyoma (ARM) is an unusual and extremely uncommon tumor . Only 96 cases have been reported.1,2 Adult rhabdomyomas are found mo st often in the region of the base of the tongue, floor of the mouth, larynx, and pharynx. Uncommon locations include the soft palate, uvula , lip and cheek, orbit, and stomach. One prior case of extension of an ARM from the supraclavicular region into the mediastinum has been des cribed as an incidental finding at autopsy.3 It is important to be awa re of and correctly identify this tumor because total excision may be curative. Follow-up must be long-term, as recurrence can occur after 3 5 years.4 The authors present a case of an ARM diagnosed during the ev aluation and treatment of a symptomatic mediastinal mass. This ARM was found to involve the esophagus and trachea from the inferior constric tors in the neck to the azygous vein in the mediastinum. This case rep resents a previously undescribed presentation of an ARM. We present a review of ARM and outline our diagnostic, therapeutic, and follow-up p lans.