Growing skull fractures occur most commonly after head injury; however
, their ''craniofacial equivalents'' may occur after neurosurgical or
craniofacial operations in pediatric patients. Experience with five se
parate cases is reviewed, including one case that involved the anterio
r cranial base and presented with vertical dystopia and proptosis. Nec
essary contributing factors appear to include (1) cranial bone defect,
(2) dural tear, and (3) expanding intracranial process (e.g., growth
of the brain). Prompt recognition and diagnosis of the problem are ess
ential to prevent the development of progressive neurological complica
tions. The pathophysiology and the principles of surgical management o
f these complex problems are explored in detail.