CARCINOMA OF THE AMPULLA OF VATER AND MESENTERIC FIBROMATOSIS (DESMOID TUMOR) ASSOCIATED WITH GARDNERS-SYNDROME - PROBLEMS IN MANAGEMENT

To date, 29 patients with Gardner's syndrome have been identified who developed carcinoma of the ampulla of Vater, and many others have been identified with mesenteric fibromatosis (desmoid tumor), but there ha ve been only four cases of Gardner's syndrome with both ampullary carc inoma and mesenteric fibromatosis reported in the world literature. Th is article focuses on the complications and major problems in manageme nt resulting from the simultaneous occurrence of these two known featu res of Gardner's syndrome: carcinoma of the ampulla of Vater and fibro matosis (desmoid tumor) of the intestinal mesentery.