A 1-MONTH-OLD INFANT with a Dandy-Walker malformation underwent the pl
acement of a ventriculoperitoneal shunt to treat progressive hydroceph
alus. On the initial computed tomographic scan, a subependymal cystic
lesion larger than 1 cm in diameter was noted in the head of the right
caudate nucleus, which enlarged to 3 cm in diameter on follow-up imag
ing studies over the course of a year. Biopsies taken at the time of f
enestration failed to show the presence of neoplasia. This appears to
be the first reported case of a cyst of this nature to show progressiv
e enlargement.