THE G-SYNDROME - OPITZ OCULO-GENITAL-LARYNGEAL SYNDROME - OPITZ BBB GSYNDROME - OPITZ-FRIAS SYNDROME/

We report on a family exhibiting a range of congenital anomalies consi stent with the G syndrome of Opitz. Three members of the family had la ryngo-tracheo-oesophageal clefts, one of which succumbed. There was a strong family history of perinatal mortality on the maternal side of t he family. We note also the paucity of reported cases of this syndrome in the otolaryngological literature and stress the necessity of early diagnosis in the management.