Extramammary Paget's disease of the vulva is an uncommon vulvar neopla
sm with a high rate of recurrence. A 64-year-old white female with a h
istory of extramammary Paget's disease of the vulva, excised in 1987 b
y skinning vulvectomy and treated again in 1993 by skinning vulvectomy
with split-thickness skin grafting, presented in 1994 with recurrent
Paget's disease in the area of the skin graft. Extramammary Paget's di
sease of the vulva may recur in an area previously totally excised and
transplanted with autologous skin. Therefore, close follow-up is nece
ssary in all patients with this pathologic entity. (C) 1995 Academic P
ress, Inc.