A case is reported of a 13 year old Kenyan girl who presented at the K
enyatta National Hospital Dental Clinic with multiple mandibular and m
axillary cysts, cutaneous lesions and mandibular prognathism. This com
bination of clinical and radiographic features led to a diagnosis of b
asal cell nevus syndrome. This paper is the first reported case of the
syndrome in Kenya. The significance of thorough clinical inspection a
nd radiographic screening of suspected cases is discussed.