We report on a patient with multi centric juvenile xanthogranuloma, wh
ose unusual clinical and histological pattern initially obscured the d
iagnosis. Spontaneous remission of the tumour, which has now been main
tained for over 2 years, the change from the primary monomorphological
fibrocytic appearance to a polymorphological histiocytic picture with
multiple fat-storing giant cells, and the lacking dermonstration of s
pecific cell organelles finally allowed the nature of the disease to t
he definitely diagnosed.