INTERNAL BRAIN HERNIATION IN A PATIENT WITH APERTS-SYNDROME

Patients with Apert's syndrome typically exhibit craniosynostosis, exo rbitism, midface hypoplasia, and symmetric syndactyly. There have also been occasional descriptions of the variable dysmorphology of the inn er surface of the calvarium. We present a patient with Apert's syndrom e who had an intracranial herniation of a portion of the frontal lobe through a ridge of ossified dura. The ridge and the gliotic cortical t issue were removed when the patient underwent repair of the hypertelor ism at age six. Bone grafts for this repair were fashioned in part fro m the resected ridge. We believe this finding may be the result of a s mall dural tear that occurred during prior surgery.