PRIMARY RENAL SARCOMA

Primary renal sarcoma represents approximately 1 per cent of all prima ry tumors of the kidney, The purpose of this study is to review the ex perience at Roswell Park Cancer Institute with the treatment of primar y renal sarcoma. Four patients with a diagnosis of primary renal sarco ma admitted from 1976 to 1983 form the basis of this review. All patie nts underwent radical nephrectomy. The tumor was localized in two pati ents, and locally invasive in two patients. All patients had recurrenc e of metastatic disease. Patients with localized disease recurred at 1 9.0 and 25.0 months respectively, Patients with invasive disease recur red at 4.0 and 5.0 months respectively. Patients presenting with local ized disease survived a mean of 34.0 months. Patients presenting with invasive disease died at 6.0 and 10.0 months from time of diagnosis, P rimary renal sarcoma is a rare entity. Only patients presenting with l ocalized disease have a reasonable chance for prolonged survival.