HISTIOCYTOSIS-X OF THE VULVA WITH A CONFUSING CLINICAL AND PATHOLOGICAL PRESENTATION - A CASE-REPORT

Histiocytosis X (HX) is It rare disorder of Langerhans cells and most commonly occurs in children. We report a ease of HX of the vulva in a 76-year-old woman that clinically simulated a yeast infection of the v ulva but histologically resembled an amelanotic melanoma. We briefly r eport the clinical and pathologic features of this case, which respond ed to vincristine followed by vinblastine and was in complete remissio n after nine months.