SURGICAL-TREATMENT OF ECTOPIA LENTIS IN C HILDREN AND YOUNG-ADULTS WITH MARFANS DISEASE

Introduction To determine the visual outcome of surgical therapy and c onservative management, we retrospectively reviewed all our patients w ith ectopia lentis and Marfans disease. Material and method Thirty-fiv e eyes of 18 patients (age 8 to 47, average 25,3) were studied. Eight eyes were followed conservatively the remaining 27 eyes underwent a le nsectomy either with the Kloti vitreous stripper (18) or using other t echniques (9). Results Over follow-up periods ranging from 0.5 to 13 y ears (average 6.2 years) low visual acuity was found in non-operated e yes. Retinal detachment occurred in 2 out of 8 eyes. Eyes undergoing o ther surgical techniques had a mean final visual acidity of 0.2. Retin al detachment occurred with high frequency (6 out of 9 eyes). Lensecto my-vitrectomy was a safe and effective procedure with a mean final vis ual acuity of 0.6. No retinal detachment or secondary glaucoma were fo und. Comment Our study suggests that performing lensectomy-vitrectomy with the Kloti vitreous stripper is the best surgical approach in ecto pia lentis with Marfan's disease. This technique allows the vitreous t o be handled more effectively and, has led to improve results.