X-LINKED FAMILIAL EXUDATIVE VITREORETINOPATHY - REPORT OF ONE FAMILY

Background: Familial exudative vitreoretinopathy is an uncommon heredo degenerative disease with different types of inheritance and degrees o f severity. Methods: Findings in five affected members of a family in which the X-linked mode of inheritance of familial exudative vitreoret inopathy is present are discussed. Results: Patients presented with ch aracteristic retinal exudative tractional detachment, temporal retinal vessel traction, capillary dilatation, neovascularization, and vitreo us veils. Conclusion: A review of the 21 cases of X-linked familiar ex udative vitreoretinopathy reported to date indicates a worse outcome i n this mode of inheritance than in cases of autosomal dominant inherit ance,