NEONATAL LUPUS SYNDROME - REPORT OF A CASE

Neonatal lupus syndrome (NLS) is characterized by the presence of cuta neous lupus, congenital heart block or both associated with maternal a utoantibodies anti-Re (SS-A) and anti-La (SS-B). NLS is responsible fo r more than 80 percent of cases with isolated congenital complete hear t block This report describes a neonate with third-degree atrioventric ular block who was born to an anti-Re (SS-A) positive mother. The derm atological and hematological manifestations of NLS were absent. The in fant's clinical condition was good during the two months of follow-up with expectant management.