ORBITAL LYMPHANGIOMA WITH INTRACRANIAL EXTENSION

We report a case of biopsy-proven orbital lymphangioma with contiguous spread intracranially in a 14-year-old boy. The patient had a history of congenital orbital lymphangioma and hydrocephalus. Multiple functi onal and cosmetic periorbital surgeries were done over the years. Seve re unresponsive amblyopia developed along with disfiguring anterior or bital and brow invasion of tumor. Since the age of 4 years, the patien t had had 12 episodes of periorbital and orbital cellulitis, often aft er upper respiratory infections. CT and MRI scans have shown progressi on of the tumor posteriorly beyond the orbital confines. The tumor, no w present in the superior and inferior orbital fissure and the paranas al sinuses, extends extradurally into the middle cranial fossa. This c ase is unique, with documentation of the benign tumor's progressive po sterior extension intracranially, along with repeated episodes of seve re periorbital cellulitis.