Accessary mammary tissue (AMT) is a minor cutaneous abnormality usuall
y located along the embryonic mammary lines which run from axillae to
the inner surface of the thighs. Ectopic AMT accounts for about 10% of
cases and may occur anywhere on the skin. We report three Caucasian p
atients presenting with mammae erraticae characterized by unusual asso
ciated findings. Case 1: a 28-year-old woman with pseudomamma on the r
ight subclavicular region and with a family history of AMT in her fath
er and two sisters. Case 2: a 25-year-old man with two pseudomammae on
e located ectopically on the left subscapular region and another on th
e left mammary line. Case 3: a 52-year-old woman with polythelia on th
e midsternal line and the concomitant presence of nephro-urinary defec
ts. Ecographic evaluation of AMT of each patient excluded the presence
of grandular tissue. The significant association between AMT and neph
ro-urinary defects indicates the need for a careful investigation of s
ubjects affected with ectopic AMT.