Cutaneous endometrisois is regarded as a rare condition. It usually oc
curs in scars after gynecological surgery, but can also develop sponta
neously. The case of a 31 year-old woman with spontaneous umbilical en
dometriosis is presented. A small nodule has appeared in the umbilicus
about 9 months before admission and had been enlarging since that tim
e. The lesion was infrequently associated with a mild pain, which was
unrelated to the menstruation. Physical examination revealed a firm, b
luish-brown nodule in the umbilical depression. Histopathology showed
glandular lumina in the dermis resembling endometrial tissue. Cutaneou
s endometriosis should be included in the differential diagnosis of um
bilical lesions, even when there is no relationship with the menses.