MALIGNANT MELANOTIC NEUROECTODERMAL TUMOR OF INFANCY

A 2-month-old boy underwent surgery for removal of a right temporal me lanotic neuroectodermal tumor of infancy (MNTI). Histologically the tu mor tissue showed signs of malignancy. The child was reexamined severa l times up to the age of 5 years. Neuroradiological evaluation showed no evidence of tumor recurrence or metastases. No resulting handicap w as observed during neurological and psychological follow-up examinatio n at the age of 5 years. Our findings confirm that surgical removal as the therapy of choice provides an excellent prognosis for this kind o f tumor in spite of its histologically malignant appearance.