OBJECTIVE AND IMPORTANCE: Accessory anterior cerebral artery (ACA), wh
ich is a type of median artery of anomalous triplicate ACA, is not rar
e, but aneurysmal formation is extremely rare. We report a rare case w
ith ruptured aneurysm arising from a distal accessory ACA. We discuss
the characteristics and causes of this type of aneurysm and classifica
tion of this anomaly. CLINICAL PRESENTATION: A 63-year-old man suddenl
y developed severe headache and then loss of consciousness and paraple
gia. Computed tomography disclosed thick and diffuse subarachnoid hemo
rrhage and interhemispheric hematoma. Subsequent bleeding occurred 2 h
ours after the first hemorrhage. Cerebral angiography disclosed a sacc
ular aneurysm arising from the distal accessory ACA. INTERVENTION: Nec
k clipping of the aneurysm was performed 22 hours after the second epi
sode, using an interhemispheric approach. CONCLUSION: Although transie
nt paraplegia occurred 8 days after onset, the patient recovered well
after surgery without neurological deficit. The characteristics of the
aneurysm arising from distal accessory ACA are considered similar to
those of distal ACA aneurysm. There is, however, some confusion regard
ing the terminology of the anterior communicating artery complex anoma
lies, which we discuss.