DOMINANTLY INHERITED DRUSEN REPRESENT MORE THAN ONE DISORDER - A HISTORICAL REVIEW

Hutchinson-Tay choroiditis, Holthouse-Batten chorioretinitis, Doyne's honeycomb familial choroiditis and Malattia levantinese are various na mes which have been used to denote dominantly inherited drusen. Whethe r these represent one or more than one disorder remains unclear becaus e of the quality of the illustrations and incomplete information in so me of the original articles. The early descriptions of these various c onditions have been reviewed. Evidence is presented that Doyne's honey comb familial choroiditis and Malattia levantinese are disorders which can be distinguished from each other by clinical criteria.