Eight patients with a chondrosarcoma of the temporal bone have been tr
eated at the National Hospital for Neurology and Neurosurgery over a 1
6-year-period. Patients usually presented with symptoms and signs of l
ower cranial nerve pulsies, though in most cases these resolved after
surgery. This result, combined with the fact long-term survival can be
achieved, makes surgical treatment of these tumours the best option,
as the response to primary radiotherapy is uncertain. Surgical access
is difficult, but an infratemporal approach is probably the most satis
factory. The use of post-operative adjuvant radiotherapy may provide s
ome benefit. Long-term follow-up is necessary, and for this magnetic r
esonance imaging (MRI) is preferable to computed tomography (CT) scann
ing.