ROSAI-DORFMAN DISEASE IS a rare idiopathic histioproliferative disease
affecting the lymph nodes. Extranodal involvement has also been recog
nized, but central nervous system manifestations are extremely rare. O
nly 12 patients with intracranial involvement have been reported previ
ously, and they all presented with clinical and radiological findings
suggestive of meningioma. We report multiple meningeal nodules in a pa
tient presenting with seizures whose pathological findings at surgery
confirmed the diagnosis of Rosai-Dorfman disease. A review of all prev
iously reported intracranial lesions is presented.