Er. Rodriguez et al., CAROLIS-DISEASE CONGENITAL LIVER FIBROSIS AND POLYCYSTIC RENAL-DISEASE - AN UNUSUAL ASSOCIATION, Revista espanola de enfermedades digestivas, 88(12), 1996, pp. 873-876
We report the case of a woman with Caroli's syndrome (Caroli's disease
and congenital hepatic fibrosis) and adult polycystic kidney disease.
Whereas the association of these two entities with autosomal-recessiv
e-polycystic kidney disease has been widely reported, its association
with adult-polycystic kidney disease is very infrecuent.