We report a baby's development with expanding cyst of the septum pellu
cidum. It was detectedaccidentally during diagnostic evaluation of epi
leptic convulsions and psychomotoric retardation. The dramatic increas
ing of the cyst was followed by cranial ultrasonography for ten months
. The progression of clinical symptoms couldn't be explained because a
fter drainage of the cyst, no improvement took place. MRT with Spectro
scopy lead to the tentative diagnosis, Morbus Alexander. This couldn't
be proved because no biopsy of the brain was performed against the de
cision of the child's mother, nor postmortal (the child died at 20 mon
ths).