MALIGNANT FIBROUS HISTIOCYTOMA OF THE RIGHT VENTRICLE OF THE HEART

Right-sided cardiac malignant fibrous histiocytoma (MFH) is extremely rare, and fo the authors' knowledge only three cases have been reporte d. In this study, a case of MFH in the right ventricle, the septum, an d the pulmonary valves and artery in a 47 year old male is described. The tumor showed typical pathological features of MFH, such as cellula r pleomorphism, storiform pattern and abundant mitoses. Immunohistoche mical and electron microscopical findings were compatible with MFH, an d excluded the possibility of leiomyosarcoma and angiosarcoma. Whole b ody examination, including Gallium scintigram, localized the primary s ite to the heart. The details of this case are presented with a review of the reported cases of cardiac MFH.