HELICAL HAIRS - A NEW HAIR ANOMALY IN A PATIENT WITH NETHERTONS SYNDROME

Authors
Citation
R. Lurie et Bz. Garty, HELICAL HAIRS - A NEW HAIR ANOMALY IN A PATIENT WITH NETHERTONS SYNDROME, Cutis, 55(6), 1995, pp. 349-352
Citations number
12
Categorie Soggetti
Dermatology & Venereal Diseases
Journal title
CutisACNP
ISSN journal
00114162
Volume
55
Issue
6
Year of publication
1995
Pages
349 - 352
Database
ISI
SICI code
0011-4162(1995)55:6<349:HH-ANH>2.0.ZU;2-E
Abstract
A new hair shaft defect, helical hair, is presented. This hair abnorma lity was found to accompany trichorrhexis invaginata and pill torti in an infant with Netherton's syndrome. The patient's main clinical feat ures included erythroderma since birth, failure to thrive, recurrent i nfections, hepatosplenomegaly, lymphadenopathy, eosinophilia, hypergam maglobulinemia, and high serum IgE levels, A possible mechanism for th e formation of helical hair is reviewed.