We present a single pericardial patch repair of the sinus venosus defe
ct with anomalously connected pulmonary veins, incorporating enlargeme
nt of the superior vena cava. In our small series to date this procedu
re has been carried out without morbidity or mortality. Noninvasive fo
llow-up by echocardiography and electrocardiography, over the short te
rm, has not detected any stenosis of the venous pathways or sinus node
dysfunction.