WILDERVANCKS SYNDROME PRESENTING AS HEMIPARESTHESIA

A 41-year-old male presented with recent-onset left hemiparesthesia, d escribed as a ''tingling numbness'' of the upper extremity, torso, and face. History revealed a lifelong horizontal diplopia, neck stiffness , and left-sided hearing loss for 5 months. Examination revealed an oc ular exam consistent with Duane's retraction syndrome, clinical and ra diographic evidence of congenital fusion of C2 and C3 demonstrative of the Klippel-Feil anomaly, and a sensorineural hearing loss confirmed by audiometry. The diagnosis of Wildervanck's syndrome was made based on this classic triad of findings. A thorough evaluation has not yield ed an objective explanation for the episodic hemiparesthesia. We prese nt a patient exhibiting the classic triad of Wildervanck's syndrome, w hose presentation is unique because hemiparesthesia has not previously been reported in association with this rare syndrome.