A leiomyosarcoma was diagnosed in the midportion of the inter-renal in
ferior vena cava. Survival was long (6 years) but required 14 reoperat
ions to remove metastases.During the first operation, vascular integri
ty was reestablished with a cava-cava prosthesis after exeresis of the
upstream cava without removal of the left renal vein ostium. The righ
t renal vein was sectioned and directly implanted onto the prosthesis.
The pathology report confirmed the diagnosis of leiomyosarcoma with m
ultiple metastases presenting cytonuclear anomalies which worsened wit
h time.