DIFFUSE PULMONARY ARTERIOVENOUS MALFORMATION IN A CHILD WITH POLYSPLENIA SYNDROME

Pulmonary arteriovenous malformation (PAVM) is usually seen as a well- circumscribed cystic mass. In this communication we describe a diffuse arteriovenous malformation in a 5-month-old infant. The lesion was se en only at the microscopic level and was associated with abdominal het erotaxy, atrial situs solitus, polysplenia, interrupted inferior vena cava, atrial septal defect, and atrioventricular canal. This uncommon association may be within the spectrum of polysplenia syndrome.