A 15-year-old boy presented with chest pain and a new heart murmur. Th
e clinical diagnosis of pulmonary stenosis was confirmed by two-dimens
ional and Doppler echocardiographic examinations. A large, encapsulate
d, partly solid and partly cystic tumor in the anterior mediastinum, v
isualized by ultrasonography, was compressing the main pulmonary arter
y and producing the right ventricular outflow tract obstruction. The t
umor was removed surgically and was found to be a benign teratoma. Pos
toperative ultrasound examination of the right ventricular outflow tra
ct showed no evidence of obstruction. We conclude that: (1) there are
subtle clinical diagnostic differences between intrinsic and extrinsic
pulmonary stenosis; (2) ultrasound examination can make cardiac cathe
terization unnecessary; and (3) relief of the extrinsic cause of pulmo
nary stenosis should be curative.